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Hypertrophic apical cardiomyopathy (Yamaguchi syndrome): decision-making tactics

https://doi.org/10.30629/0023-2149-2025-103-10-11-827-835

Abstract

The article describes apical hypertrophic cardiopathy, its etiology and pathogenesis. A clinical case of a patient with apical hypertrophic cardiomyopathy is presented. The features of the course of the disease, modern approaches to assessing the prognosis are described. The issues of differential diagnosis are considered.

About the Authors

N. I. Gulyaev
National Medical Research Center of High Medical Technologies — A.A. Vishnevsky Central Military Clinical Hospital of the Ministry of Defense of Russia; Branch of the Military Medical Academy named after S.M. Kirov of the Russian Ministry of Defense in Moscow; Patrice Lumumba Peoples’ Friendship University of Russia, Ministry of Education and Science of the Russian Federation
Russian Federation

Nikolai I. Gulyaev — Doctor of Medical Sciences, Professor, Head of the Cardiology Center of the Vishnevsky National Research Medical Center of the Russian Ministry of Defense.

Krasnogorsk; Moscow



Yu. V. Ovchinnikov
Branch of the Military Medical Academy named after S.M. Kirov of the Russian Ministry of Defense in Moscow
Russian Federation

Yuri V. Ovchinnikov — Doctor of Medical Sciences, Professor, Branch of the Federal State Budgetary Educational Institution of Higher Education named after S.M. Kirov of the Ministry of Defense of the Russian Federation in Moscow.

Moscow



N. A. Varavin
Military Medical Academy named after S.M. Kirov of the Ministry of Defense of the Russia
Russian Federation

Nikita A. Varavin — Candidate of Medical Sciences, senior resident of the Cardiology Department of the 1st Department (Advanced Medical Therapy) named after Academician N.S. Molchanov of the Federal State Budgetary Educational Institution of Higher Medical Education named after S.M. Kirov of the Ministry of Defense of the Russian Federation.

St. Petersburg



I. A. Puzhalov
Military Medical Academy named after S.M. Kirov of the Ministry of Defense of the Russia
Russian Federation

Ilya A. Puzhalov — residency student, member of the Military Scientific Society of Cadets and Trainees at the 1st Department (Advanced Medical Training Therapy) named after Academician N.S. Molchanov of the Federal State Budgetary Educational Institution of Higher Medical Education named after S.M. Kirov of the Ministry of Defense of the Russian Federation.

St. Petersburg



A. A. Santakov
Military Medical Academy named after S.M. Kirov of the Ministry of Defense of the Russia
Russian Federation

Alexandr A. Santakov — residency student, member of the Military Scientific Society of Cadets and Trainees at the 1st Department (Advanced Medical Training Therapy) named after Academician N.S. Molchanov of the Federal State Budgetary Educational Institution of Higher Medical Education named after S.M. Kirov of the Ministry of Defense of the Russian Federation.

St. Petersburg



I. A. Menkov
Military Medical Academy named after S.M. Kirov of the Ministry of Defense of the Russia
Russian Federation

Igor A. Menkov — Candidate of Medical Sciences, Head of the Department — Radiologist of the X-ray Department of Radiation Diagnostics (inpatient patients) of the Clinic of Radiology and Radiology of the Federal State Budgetary Educational Institution of Higher Medical Education named after S.M. Kirov of the Ministry of Defense of the Russian Federation.

St. Petersburg



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Review

For citations:


Gulyaev N.I., Ovchinnikov Yu.V., Varavin N.A., Puzhalov I.A., Santakov A.A., Menkov I.A. Hypertrophic apical cardiomyopathy (Yamaguchi syndrome): decision-making tactics. Clinical Medicine (Russian Journal). 2025;103(10-11):827-835. (In Russ.) https://doi.org/10.30629/0023-2149-2025-103-10-11-827-835

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ISSN 0023-2149 (Print)
ISSN 2412-1339 (Online)