clinmedКлиническая медицинаClinical Medicine (Russian Journal)0023-21492412-1339ООО «Медицинское информационное агентство»10.30629/0023-2149-2025-103-10-11-827-835clinmed-1306Research ArticleЗАМЕТКИ И НАБЛЮДЕНИЯ ИЗ ПРАКТИКИNOTES AND OBSERVATIONS FROM PRACTICEГипертрофическая апикальная кардиомиопатия (синдром Ямагучи): тактика принятия решенийHypertrophic apical cardiomyopathy (Yamaguchi syndrome): decision-making tacticshttps://orcid.org/0000-0002-7578-8715ГуляевН. И.GulyaevN. I.

Гуляев Николай Иванович — д-р мед. наук, профессор, начальник кардиологического центра ФГБУ «НМИЦ ВМТ им. А.А. Вишневского» Минобороны России.

Красногорск; Москва

Nikolai I. Gulyaev — Doctor of Medical Sciences, Professor, Head of the Cardiology Center of the Vishnevsky National Research Medical Center of the Russian Ministry of Defense.

Krasnogorsk; Moscow

nig27@mail.ruhttps://orcid.org/0000-0003-1843-087XОвчинниковЮ. В.OvchinnikovYu. V.

Овчинников Юрий Викторович — д-р мед. наук, профессор, филиал ФГБВОУ ВО «ВМедА им. С.М. Кирова» Минобороны России в г. Москве.

Москва

Yuri V. Ovchinnikov — Doctor of Medical Sciences, Professor, Branch of the Federal State Budgetary Educational Institution of Higher Education named after S.M. Kirov of the Ministry of Defense of the Russian Federation in Moscow.

Moscow

https://orcid.org/0000-0001-9389-6018ВаравинН. А.VaravinN. A.

Варавин Никита Алексеевич — канд. мед. наук, старший ординатор кардиологического отделения 1 клиники (терапии усовершенствования врачей) им. академика Н.С. Молчанова ФГБВОУ ВО «ВМедА им. С.М. Кирова» Минобороны России.

Санкт-Петербург

Nikita A. Varavin — Candidate of Medical Sciences, senior resident of the Cardiology Department of the 1st Department (Advanced Medical Therapy) named after Academician N.S. Molchanov of the Federal State Budgetary Educational Institution of Higher Medical Education named after S.M. Kirov of the Ministry of Defense of the Russian Federation.

St. Petersburg

https://orcid.org/0009-0008-2019-9615ПужаловИ. A.PuzhalovI. A.

Пужалов Илья Алексеевич — слушатель, член Военно-научного общества курсантов и слушателей при 1-й кафедре (терапии усовершенствования врачей) им. академика Н.С. Молчанова ФГБВОУ ВО «ВМедА им. С.М. Кирова» Минобороны России.

Санкт-Петербург

Ilya A. Puzhalov — residency student, member of the Military Scientific Society of Cadets and Trainees at the 1st Department (Advanced Medical Training Therapy) named after Academician N.S. Molchanov of the Federal State Budgetary Educational Institution of Higher Medical Education named after S.M. Kirov of the Ministry of Defense of the Russian Federation.

St. Petersburg

https://orcid.org/0009-0003-7761-0894СантаковА. А.SantakovA. A.

Сантаков Александр Андреевич — слушатель, член Военно-научного общества курсантов и слушателей при 1-й кафедре (терапии усовершенствования врачей) им. академика Н.С. Молчанова ФГБВОУ ВО «ВМедА им. С.М. Кирова» Минобороны России.

Санкт-Петербург

Alexandr A. Santakov — residency student, member of the Military Scientific Society of Cadets and Trainees at the 1st Department (Advanced Medical Training Therapy) named after Academician N.S. Molchanov of the Federal State Budgetary Educational Institution of Higher Medical Education named after S.M. Kirov of the Ministry of Defense of the Russian Federation.

St. Petersburg

https://orcid.org/0000-0002-1569-2180МеньковИ. А.MenkovI. A.

Меньков Игорь Анатольевич — канд. мед. наук, заведующий отделением — врач-рентгенолог рентгеновского отделения лучевой диагностики (стационарных пациентов) клиники рентгенорадиологии ФГБВОУ ВО «ВМедА им. С.М. Кирова» Минобороны России.

Санкт-Петербург

Igor A. Menkov — Candidate of Medical Sciences, Head of the Department — Radiologist of the X-ray Department of Radiation Diagnostics (inpatient patients) of the Clinic of Radiology and Radiology of the Federal State Budgetary Educational Institution of Higher Medical Education named after S.M. Kirov of the Ministry of Defense of the Russian Federation.

St. Petersburg

ФГБУ «Национальный медицинский исследовательский центр высоких медицинских технологий — Центральный военный клинический госпиталь им. А.А. Вишневского» Минобороны России; Филиал ФГБВОУ ВО «Военно-медицинская академия им. С.М. Кирова» Минобороны России в г. Москве; ФГАОУ ВО «Российский университет дружбы народов имени Патриса Лумумбы» Минобрнауки РФРоссияNational Medical Research Center of High Medical Technologies — A.A. Vishnevsky Central Military Clinical Hospital of the Ministry of Defense of Russia; Branch of the Military Medical Academy named after S.M. Kirov of the Russian Ministry of Defense in Moscow; Patrice Lumumba Peoples’ Friendship University of Russia, Ministry of Education and Science of the Russian FederationRussian FederationФилиал ФГБВОУ ВО «Военно-медицинская академия им. С.М. Кирова» Минобороны России в г. МосквеРоссияBranch of the Military Medical Academy named after S.M. Kirov of the Russian Ministry of Defense in MoscowRussian FederationФГБВОУ ВО «Военно-медицинская академия им. С.М. Кирова» Минобороны РоссииРоссияMilitary Medical Academy named after S.M. Kirov of the Ministry of Defense of the RussiaRussian Federation20251402202610310-11827835Copyright © Гуляев Н.И., Овчинников Ю.В., Варавин Н.А., Пужалов И.A., Сантаков А.А., Меньков И.А., 20262026Гуляев Н.И., Овчинников Ю.В., Варавин Н.А., Пужалов И.A., Сантаков А.А., Меньков И.А.Gulyaev N.I., Ovchinnikov Y.V., Varavin N.A., Puzhalov I.A., Santakov A.A., Menkov I.A.Данная работа распространяется под лицензией Creative Commons Attribution 4.0.This work is licensed under a Creative Commons Attribution 4.0 License.https://www.clinmedjournal.com/jour/article/view/1306

В статье описаны варианты апикальной гипертрофической кардиомиопатии, ее этиология и патогенез, клиническая картина, возможности инструментальной диагностики и тактика лечения. Представлен клинический случай пациента с апикальной гипертрофической кардиомиопатией. Описаны особенности течения заболевания, современные подходы к оценке прогноза. Рассмотрены вопросы дифференциальной диагностики.

The article describes apical hypertrophic cardiopathy, its etiology and pathogenesis. A clinical case of a patient with apical hypertrophic cardiomyopathy is presented. The features of the course of the disease, modern approaches to assessing the prognosis are described. The issues of differential diagnosis are considered.

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DOI: 10.17116/kardio2024170117Konstantinov I.E., Fricke T.A. Commentary: A paradigm change in surgical management of the apical hypertrophic cardiomyopathy to avoid heart transplantation. J. Thorac. Cardiovasc. Surg. 2024;26:S0022-5223(24)00658-5. DOI: 10.1016/j.jtcvs.2024.07.042Konstantinov I.E., Fricke T.A. Commentary: A paradigm change in surgical management of the apical hypertrophic cardiomyopathy to avoid heart transplantation. J. Thorac. Cardiovasc. Surg. 2024;26:S0022-5223(24)00658-5. DOI: 10.1016/j.jtcvs.2024.07.042Афанасьев А.В., Богачев-Прокофьев А.В., Кирилова В.С. и др. Трансапикальная миоэктомия как альтернатива трансплантации сердца у пациента с апикальной гипертрофической кардиомиопатией. Клиническая и экспериментальная хирургия. Журнал имени академика Б.В. Петровского. 2024;12(1):127-134. DOI: 10.33029/23081198-2024-12-1-127-134Afanasyev A.V., Bogachev-Prokofiev A.V., Kirilova V.S. and others. 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The authors declare that there are no conflicts of interest present.