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Cardiac amyloidosis, features of diagnosis and treatment

https://doi.org/10.30629/0023-2149-2024-102-1-27-35

Abstract

Cardiac amyloidosis is considered a rare disease, but as diagnostic capabilities increase, so does the assessment of its prevalence. Cardiac amyloidosis manifests itself with symptoms of restrictive cardiomyopathy, leading to progressive heart failure. However, the underlying pathogenetic mechanisms of the disease differ. This literature review provides an overview of cardiac amyloidosis, from classification to molecular mechanisms and modern treatment options.

About the Authors

A. V. Demyanenko
Central Military Clinical Hospital named after P.V. Mandrykа of the Ministry of Defense of Russia
Russian Federation

Alexey V. Demyanenko — Candidate of Medical Sciences, Deputy Head in medicine

Moscow



N. A. Varavin
Military Medical Academy named after S.M. Kirov of the Ministry of Defense of Russia
Russian Federation

Nikita A. Varavin — cardiologist of the 1st Department of Therapy

Saint Petersburg



A. A. Santakov
Military Medical Academy named after S.M. Kirov of the Ministry of Defense of Russia
Russian Federation

Alexander A. Santakov — student

Saint Petersburg



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Demyanenko A.V., Varavin N.A., Santakov A.A. Cardiac amyloidosis, features of diagnosis and treatment. Clinical Medicine (Russian Journal). 2024;102(1):27-35. (In Russ.) https://doi.org/10.30629/0023-2149-2024-102-1-27-35

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