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Infective endocarditis of the pulmonary valve in congenital aortopulmonary septal defect with eisenmenger syndrome
https://doi.org/10.30629/0023-2149-2026-104-4-316-322
Abstract
An aortopulmonary septal defect (APSD) is a rare congenital heart anomaly characterized by an abnormal communication between the ascending aorta and the pulmonary trunk in the presence of two distinct semilunar valves. Among septal defects, APSD is associated with the most rapid and unfavorable progression of pulmonary hypertension and Eisenmenger syndrome; in unoperated cases, mortality reaches up to 40% within the first year of life. We present a clinical case of a 49-year-old patient with congenital APSD complicated by Eisenmenger syndrome, who developed infective endocarditis of the pulmonary valve – an extremely rare combination not previously described in the literature.
About the Authors
N. E. Akhmedova
Ryazan State Medical University
Russian Federation
Russian Federation
Nazly E. kyzy Akhmedova – second-year resident in the specialty «Cardiology»
Ryazan
S. P. Filonenko
Ryazan State Medical University
Russian Federation
Russian Federation
Sergey P. Filonenko – Candidate of Medical Sciences, Associate Professor of the Department of Hospital Therapy with a course in Medical and Social Expertise
Ryazan
I. В. Glukhovets
Ryazan State Medical University
Russian Federation
Russian Federation
Ilya В. Glukhovets – Candidate of Medical Sciences, Associate Professor of the Department of Histology, Pathological Anatomy and Medical Genetics
Ryazan
S. V. Subbotin
Regional Clinical Cardiology Dispensary
Russian Federation
Russian Federation
Sergey V. Subbotin – Candidate of Medical Sciences, Head of the Cardiology Department №1 of the Ryazan Regional Clinical Cardiology Dispensary
Ryazan
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Review
For citations:
Akhmedova N.E., Filonenko S.P., Glukhovets I.В., Subbotin S.V. Infective endocarditis of the pulmonary valve in congenital aortopulmonary septal defect with eisenmenger syndrome. Clinical Medicine (Russian Journal). 2026;104(4):316-322. (In Russ.) https://doi.org/10.30629/0023-2149-2026-104-4-316-322
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